Thursday, March 19, 2015

Another Step in a Long Journey

Pure exhaustion and running on fumes, but so thankful to have had the opportunity to go to Houston yesterday for a second opinion on Easton’s heart. We started the day off with a hospital arrival time of 7:00 where we opened up the women’s pavilion for the day. Our first appointment was a comprehensive ultrasound that would scan Easton’s anatomy before going in for an MRI.  The purpose of the ultrasound and then MRI was to tell the depth and complexity of his “left side heterotaxy,” in regards to his stomach cavity organs (intestines, spleen, kidney, gall bladder, pancreas, liver, etc.). After an hour worth of ultrasound, the pediatric radiologist came in to check the images to see if we needed to proceed with the MRI. The radiologist was able to get all of the images he needed and we did not have to proceed with the MRI, which was great news and another procedure to not have to go through. He also gave us the first piece of GOOD NEWS…Easton’s heterotaxy, specifically, in his stomach cavity, is not as severe as originally diagnosed. In the original diagnosis, we were told that they believed he was missing his spleen, had mal-rotated intestines, off positioned stomach, liver, and potentially several other organs. He has a spleen (which is wonderful news because it means that he won’t have to live on penicillin his whole life, to fight off infections), his liver is slightly off positioned but not detrimental, and his intestines may need surgery to “tack-down” but it is not for certain and we won’t know until his birth. If he does need surgery for his intestines, the surgeon seemed confident that it was an easy procedure with promising outcomes for his intestinal function. Finally, some good news! We were excited to hear that what was going to be a long road of reconstructive surgeries for his “stomach cavity” organs would no longer seem to complicate his long road of reconstructive and complex and delicate heart disease surgeries.

Our big appointment with the “heart team” was scheduled to start at 1:00, and they did not waste a second in getting started with the echocardiogram. An echocardiogram is a fancy word for a heart ultrasound that looks for the detailed and specific intricacies of the heart. We had a “fellow” start the heart echo, right at 1:00, and he scanned me for over an hour, not really talking or saying much through the scan. You see, you either get a tech who can scan and talk or someone who just doesn’t talk at ALL through the entire scan. Most of you know me—which I am a talker, and I hate that awkward silence and the “mmhmming” sounds during any kind of scan. Knowing that Easton has heart disease, I hate those noises that just seem to confirm that things aren’t working and connecting like they normally should. I’d rather just chat throughout the ultrasound and the tech takes my mind off what is really happening. It makes me cringe to think that someone else is looking at Easton’s heart and thinks “These poor people…just unaware of the road ahead of them.” After the fellow came in and completed his portion of the scan, a sonographer came in and did another 45 minutes of scanning, but she was talkative AND not to mention a LSU fan and SAINTS fan. I liked her. Stephen and I enjoyed the conversation on football and just all things Louisiana. By the time that she was done scanning, I had been laying down (on back, which isn’t comfortable) for almost two hours. She left us and said the cardiologist would the come in and may want to do more scanning. We waited about ten minutes on the cardiologist and she came in and said, “I need a double shot of espresso for your baby’s heart!” It kind of made me giggle (to just take everything in stride) that a skilled cardiologist was put to the test when viewing the abnormalities and intricacies of Easton’s heart. She scanned me for another thirty minutes, and then was ready for the round table discussion. This time around, I wasn’t terribly anxious because my phone was literally going off left and right with friends’ texting me scriptures, sweet messages, and telling me how strong I was. Me…STRONG?!? But obviously that strength comes not of me, but of the Lord.

Amazingly, even though we were tired, we anxiously awaited to hear about Easton’s heart at the round table discussion. Remember, no one really said anything during the scan, so we really had no idea what we were about to hear, but we obviously knew we were still going to hear that he has heart disease. And, once the cardiologist came back in, she did confirm that Easton’s heart is so intricate and complex, and was by far one of the MOST difficult hearts to image in her entire career as a cardiologist. Stephen and I looked at each other and weren’t sure whether that was a compliment or just another indication that our little boy is beyond special and unique, which he is.
Easton’s original diagnosis was Pulmonary Atresia, MAPCAs, and a ventricle complication. His new diagnosis is just as severe and below I’ve typed out what the new diagnoses are.

First, Easton now has only a three-chamber heart (opposed to the normal 4 chambers) because his right ventricle is no longer functioning. At the original diagnosis, he had 4 working chambers, but with ventricles being disproportioned in size, it was workable. Now, however, he has lost function in his right ventricle, which is sad to hear and medically will no longer be of use. It will always sit there, unless by some miracle, be unusable and nonfunctioning. Therefore, it will put extra stress on his one working ventricle. The only bright spot we can find is that if he had to only have one functioning ventricle, we’re glad that it’s his left one because that is the more muscular one and his left ventricle will now have to work over time to process the blood flow. However, being a single ventricle baby is going to require extensive surgery and work to be done and we will just have to wait and pray for how he responds to surgery. 

Second, what was originally considered as Pulmonary Atresia, it appears (remember the heart is no larger than a strawberry, so it can be hard to see the intricacies) that he has his Pulmonary Artery but it is the more dominant artery (between that and the Aorta). Because the pulmonary seems to be much larger, the Aorta is now the artery that has been shorted in growth and is too small to function on its own. Both arteries have important jobs and with his aorta being too small to function, this will also require extensive surgery.

So, Easton doesn’t have MAPCAs or pulmonary atresia but exchanged those two types of heart disease for another two types. It’s not to say that the original diagnosis was in error, it was just that the heart was so small that they could tell that he had heart disease but the specificity of the heart disease was hard to diagnosis. The above conditions do have LONG and COMPLEX names: Dextrocardia, Double Inlet Left Ventricle, and Hypo-plastic Aorta.

Many of you are constantly asking what we need, which is continued prayers, support, and encouragement as we seek to obtain the best medical attention for our little boy. We were so impressed with the care and expertise yesterday and would ask for you to join us in praying through the logistics of delivering in Houston as well having it be Easton’s main cardiology hospital (for surgeries). We do NOT have to move there and Fort Worth can continue to be our home, but Easton will just need a cardiologist here to see on a routine basis, pending he responds well to surgery. I will have to relocate to Houston at 36 weeks and stay there until he is born, and then we will be there until after his first surgery. All of this is very new, so we would love for you to join us in praying over the logistics of what and how life will look like for us, as Stephen continues to work and I anxiously wait the arrival of sweet Easton.

Easton will need surgery within the first 6 days of his life. It will be a major, complex, delicate, and risky surgery because it is an in-cardiac procedure. We don’t want to make speculations or even look at percentage rates for surgery rates of success/failure, but we desperately cling to the truth that God is good and He knows and holds our future, and Easton’s. On the way out of the door, the cardiologist said, “I can see how excited you both are to have this baby,” and that’s the honest truth. We are excited to be parents, to experience parenthood, and to take peace in the fact that God handpicked us to be Easton’s parents.  It’s difficult on days like yesterday and even today to know that our sweet little boy is going to have complications that are seem unfair for any infant/adult to have to endure.

We will go back to Houston in 3 weeks to do another follow up echocardiogram to make sure that his heart is continuing to grow and “have flow” so that will be another big appointment day. For those of you who consider yourselves our prayer warriors, you can specifically be praying for that over the next three weeks—that his heart and body would continue to grow and his heart would maintain the current state that it is in or be improved.

So, obviously a lot went down yesterday; we received more “news” and then good news about his other organs. Thank you to all of you who have invested a piece of your life into Easton’s journey. Stephen and I are honestly able to have strength that is beyond us through the Lord but is tangible through the love, support, encouragement, and prayers of so many.

  


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